
Dr. Ernest Beutler
(Sep. 30, 1928 – Oct. 5, 2008)

Dr. Ernest Beutler, who first identified the G6PD enzyme deficiency in 1953, the man who was most instrumental in establishing this Web site back in 1996, a giant among scientists and a most generous, gracious person, passed away on October 5. See obituaries in The Los Angeles Times and The New York Times. A more detailed biography on Wikipedia. To read some of his articles, turn to our list of Research Papers.
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DRUGS AND FOODSTUFF TO AVOID
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[ Drug names in red are of high risk to all deficiency types. ]
| Name |
Molecular Forumla |
Risk Level j |
For whom |
|
Acetanilide (acetanilid)
|
C8 H9 N O |
High
|
Medit., Asian
|
|
Acetylphenylhydrazine (2-Phynylacetohydrazide)c
|
C8 H10 N2 O |
High
|
All
|
|
Aldesulfone sodium (sulfoxone)
|
C14 H14 N2 Na2 O6 S3 |
High
|
All
|
|
Aminophenazone (aminopyrine)
|
C13 H17 N3 O |
Low
|
All
|
|
Antazoline (antistine)
|
C17 H19 N3 |
Low
|
All
|
|
Arsinec
|
As-H3 |
High
|
All
|
|
Ascorbic Acid
|
C6 H8 O6 |
Low
|
All
|
|
Beta-Naphthol (2-Naphthol)
|
C10 H8 O |
High
|
All
|
|
Chloramphenicol
|
C11 H12 C12 N2 O5 |
High
|
Medit., Asian
|
|
Chloroquined
|
C18 H26 Cl N3 |
High
|
Medit., Asian
|
|
Ciprofloxacinb
|
C17 H18 F N3 O3 |
High
|
Medit., Asian
|
|
Colchicine
|
C22 H25 N O6 |
Low
|
All
|
|
Dapsone (diaphenylsulfone)c
|
C12 H12 N2 O2 S |
High
|
All
|
|
Dimercaprol
|
C3 H8 O S2 |
High
|
All
|
|
Diphenhydramine (difenilhydramine)
|
C17 H21 N O |
Low
|
All
|
|
Dopamine (L-dopa)
|
C8 H11 N O2 |
Low
|
All
|
|
Doxorubicin
|
C27 H29 N O11 |
High
|
Medit., Asian
|
|
Furazolidone
|
C8 H7 N3 O5 |
High
|
All
|
|
Glibenclamideb
|
C32 H28 Cl N3 O5 S |
High
|
Medit., Asian
|
|
Glucosulfone (glucosulfone sodium)
|
C24 H34 N2 Na2 O18 S3 |
High
|
All
|
|
Isobutyl Nitrite
|
C4 H9 N O2 |
High
|
Medit., Asian
|
|
Isoniazid
|
C6 H7 N3 O |
Low
|
All
|
|
Menadiol Sodium Sulfate (Vitamin k4 sodium sulfate)f
|
C11 H8 Na2 O8 S2 |
High
|
All
|
|
Menadione (menaphtone)f
|
C11 H8 O2 |
High
|
All
|
|
Menadione sodium Bisulfite (Vitamin K3 sodium bisulfite)f
|
C11 H8 O2 NaHSO3 |
High
|
All
|
|
Mepacrine (Quinacrine)
|
C23 H3O Cl N3 O |
High
|
Medit., Asian
|
|
Mesalazine - 5-Aminosalicylic Acid (paraminosalicylic acid)
|
C7 H7 N O3 |
High
|
Medit., Asian
|
|
Methyltioninium Chloride (methylene blue)
|
C16 H18 Cl N3 S |
High
|
All
|
|
Nalidixic Acidb
|
C12 H12 N2 O3 |
High
|
Medit., Asian
|
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Naphtalene, Pure (naphtalin)
|
C10 H8 |
High
|
All
|
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Niridazole
|
C6 H6 N4 O3 S |
High
|
All
|
|
Nitrofural (nitrofurazone)
|
C6 H6 N4 O4 |
High
|
All
|
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Nitrofurantoin
|
C8 H6 N4 O5 |
High
|
All
|
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Norfloxacin
|
C16 H18 F N3 O3 |
Low
|
All
|
|
O-Acetylsalicylic Acid (acetylsalicylic acid)a
|
C9 H8 O4 |
High
|
Medit., Asian
|
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Oxidase, Urate (urate oxidase)
|
|
High
|
Medit., Asian
|
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Pamaquine
|
C42 H45 N3 O7 |
High
|
All
|
|
Para-Aminobenzoic Acid (4-Aminobenzoic Acid)
|
C7 H7 N O2 |
Low
|
All
|
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Paracetamol (acetaminophen)
|
C8 H9 N O2 |
Low
|
All
|
|
Pentaquine
|
C18 H27 N3 O |
High
|
All
|
|
Phenacetin (acetophenetidin)e
|
C10 H13 N O2 |
High
|
Medit., Asian
|
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Phenazone (antipyrine)
|
C11 H12 N2 O |
Low
|
All
|
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Phenazopyridine
|
C11 H11 N5 |
High
|
Medit., Asian
|
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Phenylbutazone
|
C19 H20 N2 O2 |
Low
|
All
|
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Phenytoin
|
C19 H20 N2 O2 |
Low
|
All
|
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Phynylhydrazinec
|
C6 H8 N2 |
High
|
All
|
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Phytomenadione (Vitamin K1)
|
C31 H46 O2 |
Low
|
All
|
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Primaquineg
|
C15 H21 N3 O |
High
|
All
|
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Probenecid
|
C13 H19 NO4 S |
High
|
All
|
|
Procainamide
|
C13 H21 N3 O |
Low
|
All
|
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Proguanil (chlorguanidine)
|
C11 H16 Cl N5 |
Low
|
All
|
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Pyrimethamine
|
C12 H13 Cl N4 |
Low
|
All
|
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Quinidine
|
C20 H24 N2 O2 |
Low
|
All
|
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Quinine
|
C20 H24 N2 O2 |
Low
|
All
|
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Stibophen (2-(2-Oxido-3,5-Disulphonatophenoxy)-1,3,2,Benzodioxastibole-4-6-Disulphonate)
|
C12 H4 Na5 O16 S4 Sb |
High
|
All
|
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Streptomycin
|
C21 H39 N7 O12 |
Low
|
All
|
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Sulfacetamide
|
C8 H10 N2 O3 S |
High
|
All
|
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Sulfacytine
|
C12 H14 N4 O3 S |
Low
|
All
|
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Sulfadiazine
|
C10 H10 N4 O2 S |
Low
|
All
|
|
Sulfadimidine
|
C12 H14 N4 O2 S |
High
|
All
|
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Sulfafurazole (sulfafurazone, sulfisoxazole)
|
C11 H13 N3 O3 S |
High
|
Medit., Asian
|
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Sulfaguanidine
|
C7 H10 N4 O2 S |
Low
|
All
|
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Sulfamerazine
|
C11 H12 N4 O2 S |
Low
|
All
|
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Sulfamethoxazoleh
|
C10 H11 N3 O3 S |
High
|
All
|
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Sulfamethoxypyridazine
|
C11 H12 N4 O3 S |
Low
|
All
|
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Sulfanilamide (Sulphanilamide)
|
C6 H8 N2 O2 S |
High
|
All
|
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Sulfapyridine
|
C11 H11 N3 O2 S |
High
|
All
|
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Sulfasalazine, Salazosulfapyridine (salazopyrin)
|
C18 H14 N4 O5 S |
High
|
All
|
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Thiazosulfone (thiazolesulfone)
|
C9 H9 N3 O2 S2 |
High
|
Medit., Asian
|
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Tiaprofenic Acid
|
C14 H12 O3 S |
Low
|
All
|
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Tolonium Chloride, Tolonium Chloride (toluidine blue)
|
C15 H16 Cl N3 S |
High
|
All
|
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Trihexyphynidyl (benzhexol)
|
C20 H31 N O |
Low
|
All
|
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Trimethoprimk
|
C14 H18 N4 O3 |
Low
|
All
|
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Trinitrotoluene (2,4,6-Trinitrotoluene)
|
C7 H5 N3 O6 |
High
|
Medit., Asian
|
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Tripelennamine
|
C16 H21 N3 |
Low
|
Medit., Asian
|
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The Association is affiliated with UNIAMO, Italian Federation for Rare Diseases, which in turn is member of EURORDIS, European Organization for Rare
Diseases.
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